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Pathways of ammonia detoxification to GLN in muscles linked to Increased use from the BCAA and α-KG (cataplerosis) and proposed outcomes of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Favourable effect of BCAA on ammonia detoxification to GLN could possibly be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phe